Term
Which Dr. Barlizo packet, need to know and differential among the diseases? |
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Definition
MS, Cerebral palsy, poliomyelitis, peripheral neuropathy, charcot-Marie-Toothh, Dejerine Scottas Disease, Friedreeichs' ataxia, roussy levy syndrome, spinal dysraphism, refsum's disease, muscular dystrophy |
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Term
Which of the following disorder have the following characters: weakness and secondary muscle contracture most common sex linked inherited myopathy diagnosed early childhood delayed milestones confused with CP Found in boys only |
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Definition
Muscular dystrophy Dunchenne's |
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Term
Which of the following disorder have the following characters:
Calf muscle large and firm Due to fatty conversion Delayed walking Trendelenburg gait Grower's maneuver No sensory deficits Progressive muscle weakness Cardiac involvement Children usually wheelchair bound, early dealth due to pulmonary/cardiac disease |
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Definition
Muscular dystrophy Dunchenne's |
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Term
Which of the following disorder have the following characters:
Failure of the mesoderm and neuroectoderm to fuse and form the neural tube Spina bifida Spina bifida occulta Spina bifida cystica Leg weakness Equinovarus position of foot Diminished DTR's, sensory loss feet Associated with congenital abnormalities and mentally challenged |
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Definition
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Term
Which of the following disorder have the following characters:
Clinically manifests as a spastic deformity Inherited autosomal dominant No sensory component |
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Definition
Hereditary Spastic Paraplegia |
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Term
Which of the following disorder have the following characters:
Caused by abnormal lipid metabolism Accumulation of phytanic acid in the serum up to 50 times than normal Associated findings Peripheral muscle weakness, areflexia, dropfoot, pes cavus and claw toes |
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Definition
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Term
Which of the following disorder have the following characters:
similar to CMT addition of an essential tremor, predominately expressed in the hands Familial, slowly progressive, symmetrical neuromuscular disease Areflexia, intrinsic pedal muscle atrophy, pes carvus, claw toes, clumsy gait, poor equilibrium and essential tremor Severe alterations in nerve conduction and sensory dysfuntion |
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Definition
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Term
Which of the following disorder have the following characters:
Rare Spinocerebellar degeneration causing hypertonicity and ataxia Caused autosomal recessive inheritance Onset childhood or adolescence Hallmark: ataxia, cavus foot, claw toes, kyphoscoliosis Weakness LE: anterior and lateral compartment Imparied muscle co-cordinationn, sensory impairment function is progressive Spinal cord and peripheral nerve degeneration Loss of DTR, SOB, palpatations, heart disease EMG, NCV, ECHO, glucose levels |
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Definition
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Term
Which of the following disorder have the following characters:
Most commoninherited sensorimotor symmetrical neuropathy Begins late childhood Slowly progressive Autosomal dominant trait Neurological deficits symmetrical Progressive distal muscle wasting and weakness Areflexia Cavovarus deformity Drop foot Calf atrophy "stork leg" or "champagne bottle" Steppage gait Progressive atrophy of distal UE Diminished sensation in stocking glove distribution NCV delayed Muscle weakness begins foot intrinsics |
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Definition
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Term
Which of the following disorder have the following characters:
Similar to CMT but more severe Autosomal recessive or dominant Progressive disease leading to severe disability Onset early childhood to early adulthood Distal weakness and sensory loos of primary the lower extremity, decreased DTR's Peripheral nerves are enlarged and palpable due to "onion bulb" formaiton of the nerve Nerve biopsy: concentric proliferation of Schwann cells around area of demyelination |
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Definition
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Term
What is the diagnosis for Cerebral Palsy? |
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Definition
Based on delayed milesstones History of low birth weight Prematurity Trauma, asphyxia |
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Term
Which conditions carried the following characters: b/1 LE spasticity, scissoring gait, variable mental impairment |
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Definition
Cerebral Palsy Spastic diplegia |
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Term
Which conditions carried the following characters:
severe b/1 UE/LE spasticity, severe interllectual impairment |
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Definition
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Term
Which conditions carried the following characters:
unilateral spastic hemiparesis, less severe mental impairment |
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Definition
Spastic hemiplesia Cerebral palsy |
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Term
Which conditions associated lower extremity manifestations:
Drop foot: excessive strong Posterior muscle and weakness of dorsiflexors Shortening gastrocsoleus muscle along with contracture of posterior capsule of the ankle and STJ and thickening of the neck of the talus, creates a fixed ankle equinus |
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Definition
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Term
Which conditions associated lower extremity manifestations:
Equinus deformity Manifests as toe walking in younger child Back heeled gait in older child Equinovalgus deformity: diplegia (form of quadriplegia legs> arm) spasticity Peroneal/gastrocsoleus muscles Equinovarus deformity: hemiplegia |
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Definition
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Term
Which of the following disorder have the following characters:
Anterior horn cells from a viral infection Flaccid paralysis of those muscles innervated by those cells Extent of paralysis variable based on number of muscle affected Brainstem: respiratory muscles become paralyzed |
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Definition
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Term
Which of the following disorder have the following characters:
Paralyzed muscle is replaced by fibrous tissue L2-S1, paralysis common LE Arm involvement Limb length discrepancies |
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Definition
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Term
Which conditions with the following transmission:
Fecal-hand-oral transmission, person to person Virus is shed in oral secretions for several weeks, in feces for several months Introduced into the household by children not yet toilet trained Speads rapidly, can affect entire house hold in 4-5 days |
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Definition
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Term
Which of the following disorder have the following characters:
severe genu recurvatum occurs to avoid collapse of the knee during stsnding due to weakness of the quadriceps Ankle instability/drop foot results from weak anterior leg group muscles |
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Definition
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Term
Which of the following disorder have the following characters:
neuropathies combination of weakness along with numbness Sometimes confused with myopathic disease since both result in varying degrees of weakness or absent reflexes |
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Definition
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Term
Which condition associate with:
anatomical: weakness distal m., gps DF/ intrinsics Sensory: worse than motor loss Atrophy: Calfs, hand, feet DTR: diminished Example: DM neuropathy, CMT, gullian barre |
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Definition
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Term
Which condition associate with:
Anatomical: weakness prox m. pelvic/pectoral gp Sensory: Intact Atrophy: Pseudoatrophy calfs fibrous tissue and fat replacing muscle DTR: normal Examples: muscular dystrophy |
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Definition
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Term
Which condition associate with:
Chronic immune demyelinating disease of the CNS Characterized pathologically by plaques of inflammation, demyelination disseminated in different area of the CNS
Signs and symptoms depend on location of the lesions within brain and spinal cord
Spasticity: spastic paraparesis most common motor abnormality Stiffness, cramps, weakness and motor fatigability Flexor, extensor and adductor spasms occur with more severe dysfunction Motor symptoms worsen with elevation in body temperature Mechanism: variable conduction block in partially demylinated pathways |
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Definition
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Term
Which of the condition associate with sensory manifestations:
Numbness paresthesia Vertigo Blurred vision Diminished Hearing |
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Definition
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Term
Which of the sensory associate with:
Posterior column Dorsiflex and plantarflex 1st MPJ Ask patient to identify position with eyes closed |
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Definition
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Term
Which of the sensory associate with:
Assesses lateral spinothalamic tract intergrity |
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Definition
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Term
WHich of the following reflexs showed:
Stroke lateral aspect of rom proximal to distal then across metatarsal heads Fanning of the digits Upper motor neuron lesion |
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Definition
Babinskin sign-externsor-plantar sign-superficial reflexes |
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Term
WHich of the following reflexs showed:
Flexor withdrawal reflex should be elicited if a noxious stimulus is applied to the hallux If the hallux extends towards the noxious stimuli, indicates a pyramidal tract lesion |
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Definition
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Term
Paterllar deep tendon reflexes |
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Definition
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Term
Achilles deep tendon reflexes |
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Definition
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Term
Which of sensory deficit show the following signs?
Inability to determine a simple object placed in the palm of a patient's hand with eyes closed or by pressing an object against the plantar aspect of the foot
May reflect parietal lobe lesion |
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Definition
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Term
Which of sensory deficit show the following signs?
the ability to distinguish between letters and numbers traced onto the palm of the hand with eyes closed |
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Definition
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Term
Which of sensory deficit show the following signs?
Anterior spinothalamic tracts and the posterior collumn
Cotton ball, monofilament, brush Along dermatomes, distribution of a nerve |
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Definition
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Term
Which of sensory deficit show the following signs?
Posterior columns tuning fork over bony prominences Quantitatively using Biothesiometer |
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Definition
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