Term
| What is the formula for Mentzer's Index? |
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Definition
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Term
| What does a Mentzer's Index > 13.5 indicate? |
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Definition
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Term
| What does a Mentzer's index < 13 indicate? |
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Definition
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Term
| What calculation indicates whether the bone marrow is responding properly to the anemia? |
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Definition
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Term
| What does an RPI > 3 mean? |
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Definition
| increased production indicating hemolysis or blood loss |
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Term
| What does an RPI < 2 mean? |
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Definition
| decreased production or ineffective production for the degree of anemia |
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Term
| What type of anemia is described as Hypochromic/microcytic anemia with a low reticulocyte count and elevated red cell distribution width (RDW)? |
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Definition
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Term
| In what type of infants is iron deficiency anemia MOST COMMON? |
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Definition
| in bottle-fed infants who receive large amounts of cow’s milk (Ages 9-24mo) |
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Term
| What is the MC type of Anemia in PEDs? |
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Definition
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Term
| With what type of anemia does spooning of the finger nails occur? |
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Definition
| In SEVERE iron deficiency anemia |
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Term
| Pt presents with pallor, irritability, anorexia, tachycardia, cardiac dilation and systolic murmurs, splenomegaly and pica. What condition do you suspect? |
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Definition
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Term
| What lab value is the 1st to fall in iron deficiency anemia? |
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Definition
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Term
| What is the treatment for iron deficiency anemia? |
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Definition
| Supplementation with 3-6 mg/kg of elemental iron in three divided doses for at least 4-6 weeks |
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Term
| Which lab value for iron deficiency anemia is an acute phase reactant? |
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Definition
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Term
| When do the total body iron stores begin to decrease in an infant? How is this corrected? |
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Definition
| begin to decline after 6 mo old; add iron to their diets |
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Term
| What lab value is caused by an accumulation when the conversion of protoporphyrin to heme is blocked? What condition is it elevated in? |
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Definition
| Free Erythrocyte Protoporphyrin; Elevated in iron deficiency anemia |
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Term
| After two weeks of treating iron deficiency anemia with iron supplementation, if there is no change in lab values, what should you suspect? |
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Definition
Blood Loss
Development of Infection
Poor Compliance
Other causes of microcytic anemia |
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Term
| Pt has high TIBC, low serum ferritin, High free erythrocyte protoporphyrin, normal Hgb A or F, High RDW, Anisocytosis and Poikilocytosis. What condition do you suspect? |
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Definition
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Term
| Pt presents with normal or increased free erythrocyte protoporphyrin, High B-thalessemia and Normal A-thalassemia and a normal RDW with a Mentzer's index < 13. What condition do you suspect ? |
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Definition
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Term
| What factor is deficient in Hemophilia A? |
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Definition
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Term
| Pt presents with delayed blood clotting after trauma, hemarthrosis, retroperitoneal hematomas and CNS bleeds w/out trauma. Labs show a prolonged PT & PTT. What condition do you suspect? |
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Definition
| Hemophilia A - Factor VIII Deficiency |
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Term
| Pt presents with delayed blood clotting after trauma, hemarthrosis, retroperitoneal hematomas and CNS bleeds w/out trauma. Labs show a prolonged PTT. What condition do you suspect? |
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Definition
| Hemophilia B - Factor IX Deficiency |
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Term
| What factor is deficient in Hemophilia B? |
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Definition
| Factor IX (Christmas Factor) |
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Term
| Pt presents with minor bleeding coagulopathies such as spontaneous bleeding and hemarthroses and prolonged PTT? |
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Definition
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Term
| Treatment for Hemophilia A? |
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Definition
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Term
| What is the treatment for Hemophilia B? |
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Definition
| Factor IX, FFP or cryoprecipitate |
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Term
| What is the treatment for Factor XI deficiency? |
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Definition
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